8 results
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
specific) COMMON CLINICAL ... • Essential Criteria ... : Clinical/radiologic ... 2019 ACR/EULAR Criteria ... #Management #Rheumatology
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
Clinical history ... + cells" Treatment ... Glucocorticoids (0.6 mg/kg ... Disease #diagnosis #management ... #rheumatology
Autoimmune Hepatitis

Clinical Presentation
 - Highly variable clinical presentation, from subclinical disease to acute liver failure.
 -
Highly variable clinical ... Viral) Management ... regarding need for treatment ... AIH #Diagnosis #Management ... #Hepatology
Guillain-Barre Syndrome - Summary

Acute AIDP that presents with rapidly progressive flaccid weakness

Epidemiology:
 • 1-2 cases/100,000 per
Guillain-Barre Clinical ... : Due to nerve root ... equina • GQ1b IgG ... Syndrome #diagnosis #management ... #treatment #neurology
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Fever is the main clinical ... Histopathologic criteria ... Treatment: • Corticosteroids ... Syndrome #Diagnosis #Management ... #Hematology #Rheumatology
Hodgkin's Lymphoma Overview

Hodgkin's lymphoma (HL) is an uncommon hematological malignancy arising from mature B cells. It
Hodgkin Lymphoma - Clinical ... through Ann Arbor criteria ... Hodgkin Lymphoma Treatment ... classification #hematology ... #oncology #management
Clarkson’s Disease - Capillary leak syndrome
Epidemiology: Roughly 150 published cases, Median age 50 years, No sex
Relapsing-remitting course +++ Clinical ... Monoclonal gammopathy (IgG ... ) • IVIg 2 g/kg ... syndrome #diagnosis #management ... #rheumatology
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
recognition and management ... Clinical Presentation ... Diagnostic Criteria ... of 8 HLH-2004 criteria ... #Hematology #HemeOnc