8 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... ): Inflammatory ... (Clinical Dx). ... Eye involvement (uveitis ... inhibitors • Uveitis
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... disease: Uveitis ... Abnormal pathergy test ... Most Common Clinical ... disease (e.g. uveitis
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
, and ocular inflammation ... ulcers, cutaneous, ocular ... Uveitis, chorioretinitis ... : Ocular inflammatory ... interstitial keratitis, uveitis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Necrotizing, pauci-immune ... respiratory tracts Immune ... : - Ocular inflammatory ... lesions-interstitial keratitis, uveitis ... retinopathy Lab Tests
Immune Reconstitution Inflammatory Syndrome - Overview of IRIS

What Is IRIS?
	• A state of hyperinflammatory response that
Inflammatory Syndrome ... worsening of that disease ... skin lesions, ocular ... Zoster flare, ocular ... recovery uveitis
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
Rheumatic pain Clinical ... Diagnosis: • A clinical ... sites such as the collar ... blockers had the best ... osteoarticular and skin disease
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
) Suspect: Clinical ... photosensitivity, inflammatory ... Erythematous, macular ... context of primary immune ... Clinical Features
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
the most common clinical ... chondritis • Inflammatory ... chondritis • Ocular ... conjunctivitis, keratitis, uveitis ... tests for (not