10 results
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
disease: Uveitis ... or retinal vasculitis ... Abnormal pathergy test ... Most Common Clinical ... disease (e.g. uveitis
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... ): Inflammatory ... (Clinical Dx). ... Eye involvement (uveitis ... inhibitors • Uveitis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
: • Behçet Syndrome ... • Cogan Syndrome ... : - Ocular inflammatory ... lesions-interstitial keratitis, uveitis ... retinopathy Lab Tests
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
• Behcet syndrome ... Uveitis, chorioretinitis ... • Cogan syndrome ... : Ocular inflammatory ... interstitial keratitis, uveitis
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Autoimmune ANCA vasculitis ... life-threatening diseases ... hematuria) • Inflammatory ... , uveitis, episcleritis ... anti-GBM) Other tests
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
) Suspect: Clinical ... photosensitivity, inflammatory ... Erythematous, macular ... ANCA-associated vasculitis ... Clinical Features
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... (COVID-19) • Inflammatory ... pulmonary emboli, and ocular ... Diagnosis: • + Clinical ... Antiphospholipid syndrome
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
Rheumatic pain Clinical ... Diagnosis: • A clinical ... sites such as the collar ... blockers had the best ... osteoarticular and skin disease
Immune Reconstitution Inflammatory Syndrome - Overview of IRIS

What Is IRIS?
	• A state of hyperinflammatory response that
Syndrome - Overview ... worsening of that disease ... skin lesions, ocular ... Zoster flare, ocular ... immune recovery uveitis
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
the most common clinical ... chondritis • Inflammatory ... chondritis • Ocular ... conjunctivitis, keratitis, uveitis ... tests for (not