15 results
Lab patterns seen in Inborn Errors of Metabolism

A table of lab values compiled from UpToDate and
Inborn Errors of Metabolism ... diagnosing acute metabolic ... See IEM schema for ... metabolicemergency-pathophysiology-differential-pediatrics-metabolism-algorithm-diagnosis ... #InbornErrors #Metabolism
A schema of the pathophysiology of the inborn errors of metabolism, excluding complex storage diseases. Helps
inborn errors of metabolism ... presentations in acute metabolic ... #Pediatrics #Metabolism ... #Diagnosis #Algorithm ... #Differential #
Hypokalemia - Differential Diagnosis Algorithm
Extra-renal Losses:
 • Normal Acid-Base: Low intake
 • Metabolic acidosis: Gl tract
Hypokalemia - Differential ... Diagnosis Algorithm ... intake • Metabolic ... Gl tract loss (Diarrhea ... Renal Losses: • Metabolic
Metabolic Alkalosis - Differential Diagnosis Algorithm - Urinary Chloride
 • Cl- responsive metabolic alkalosis
Metabolic Alkalosis ... Cl- responsive metabolic ... Post-hypercapneic metabolic ... Cl- resistant metabolic ... - Normal/low
Hypokalemia Differential Algorithm
Acidosis
 - RTA
 - Diarrhea
pH Normal 
 1. Decreased Mg 
 2. Intracellular Shift
Hypokalemia Differential ... Algorithm Acidosis ... - RTA - Diarrhea ... Metabolic alkalosis ... #Causes #Workup
Metabolic Alkalosis - Urinary Chloride Algorithm
Cl- responsive metabolic alkalosis
 • Kidney loss of Cl-
Metabolic Alkalosis ... Urinary Chloride Algorithm ... Cl- responsive metabolic ... alkalosis • Normal/low ... #nephrology #differential
Hypochloremia - Differential Diagnosis Algorithm

Cause - Decreased Intake:
 • Low salt in diet
 • Exclusive D5W
Decreased Intake: • Low ... Excessive vomiting - Metabolic ... NGT suction - Diarrhea ... increase may cause metabolic ... decrease may cause metabolic
Normal Anion-Gap Acidosis (NAGMA) - Differential Diagnosis Framework and Workup

NAGMA
- Chem, ABG or VBG
- Calculate Anion
Acidosis (NAGMA) - Differential ... Framework and Workup ... Loss of HCO3 - Diarrhea ... NonAnionGap #Acidosis #Metabolic ... #Diagnosis #Workup
Hypokalemia Evaluation Algorithm

Before evaluating hypokalemia, life threatening complications such as arrhythmias and paralysis should be looked
Hypokalemia Evaluation Algorithm ... Laxative use • Diarrhea ... Pressure: - Metabolic ... Hippurate - Metabolic ... #differential #
Approach to Acid Base Disorders - Evaluation and Differential Diagnosis
1) Start with the Anion Gap (AG).
2)
• Anion Gap Metabolic ... Non-Anion Gap Metabolic ... Bicarb shift • Metabolic ... Compensatory for Metabolic ... Disorders #Evaluation #workup