10 results
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
Hemophagocytic Lymphohistiocytosis ... accumulation of clinical ... Assessment • Clinical ... Cellular immune deficiency ... #diagnosis #management
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
Hemophagocytic Lymphohistiocytosis ... : Overwhelming clinical ... syndrome associated ... age, however the disease ... #diagnosis #management
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
haemophagocytic lymphohistiocytosis ... Clinical Presentation ... • HLH Labs: ... Treatment: • Corticosteroids ... #Diagnosis #Management
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
Hemophagocytic Lymphohistiocytosis ... HLH is a critical ... ▪ Autoimmune diseases ... Clinical Presentation ... #Lymphohistiocytosis
Refeeding Syndrome Overview

What Is It?
	• Electrolyte/fluid shifts caused by initiation of nutrition in severely malnourished patient.
may cause severe clinical ... due to chronic disease ... Palpitations • Diarrhea ... • Vitamin D deficiency ... hyperparathyroidism Treatment
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
common in Asia • HLA-B51 ... association • M > F Clinical ... (Clinical Dx). ... Arthritis, AS Treatment ... #diagnosis #management
Vitamin B12 (Cobalamin) Deficiency
Etiology:
 • Vit B12 - aka cobalamin. Present in foods derived from animal
intrinsic factor, IF) Clinical ... tongue), abd pain, diarrhea ... to IBD, celiac disease ... Check for IF ab Treatment ... #diagnosis #management
Multiple Sclerosis - Summary

Multiple Sclerosis (MS) is an autoimmune-mediated neurodegenerative disease of the central nervous system
neurodegenerative disease ... • Or brainstem syndromes ... Constipation, Diarrhea ... stimulation Clinical ... sclerosis #diagnosis #management
Clinical Feature of Hypomagnesemia and Magnesium Deficiency
 • Electrolyte Disturbance: Hypokalemia, Hypocalcemia
 • Neuromuscular and central
Clinical Feature ... Atherosclerotic vascular disease ... Chronic fatigue syndrome ... signs #symptoms #Treatment ... #management #Magnesium
Gitelman Syndrome Overview

What?
• Inherited (AR) hypokalemic salt-losing tubulopathies affecting the thiazide-sensitive sodium chloride cotransporter
• Gitelman's syndrome
tubule (DCT) Clinical ... • Autoimmune disease ... Congenital chloride diarrhea ... Rhabdomyolysis Treatment ... diagnosis #nephrology #management