1979 results
Frequencies of organisms isolated according to site of infection in retrospective series of 268 patients with
patients with CGD ... infections in CGD ... DOI: 10.1093/cid ... febrilepodcast.com] #CGD ... granulomatous #disease
CGD and Mulch Pneumonitis
This acute fulminant invasive fungal pneumonia in absence of iatrogenic or exogenous immunosuppression
CGD and Mulch Pneumonitis ... associated with CGD ... febrilepodcast.com] #CGD ... granulomatous #disease
Important organisms in Chronic Granulomatous Disease (CGD):
 - Staph aureus
 - Serratia marcescens
 - Burkholderia cepacia
Granulomatous Disease ... (CGD): - Staph ... febrilepodcast.com] #CGD ... Granulomatous #Disease
Diagnosis of Chronic Granulomatous Disease (CGD):
 - Neutrophil function tests (DHR123, NBT)
 - Genotyping confirmation

gp91phox is
Granulomatous Disease ... (CGD): - Neutrophil ... Granulomatous #Disease ... #CGD #diagnosis
Chronic granulomatous disease and the phagocyte respiratory burst
NADPH oxidase

By Dr. Sara Dong @swinndong via Febrile [febrilepodcast.com]

#CGD
granulomatous disease ... febrilepodcast.com] #CGD ... granulomatous #disease
Liver abscesses are unique in setting of chronic granulomatous disease

By Dr. Sara Dong @swinndong via Febrile
granulomatous disease ... febrilepodcast.com] #CGD
Invasive Aspergillus (IA) - Diagnosis and Management
Aspergillus is ubiquitous in nature. Most invasive infections are caused
Advanced HIV/AIDS, CGD ... vori Infectious Diseases
Fungal Biomarkers: Beta-D-Glucan and Aspergillus Galactomannan
Beta-D-Glucan:
 • Polysaccharide cell wall component of many fungi
 • Pathogens:
colonization vs invasive disease ... SOT recipients, CGD
Upper GI Bleed - Management Algorithm

Upper GI bleed Suspected: Melena, hematemesis, coffee-ground emesis, BRBPR
Initial Stabilization
Concern for
Concern for Liver Disease ... Consult GI ± EGD ... • Peptic Ulcer Disease ... idiopathic, liver, CTD
Diagnostic algorithm for a child or adolescent with suspected pulmonary hypertension. CHD, congenital heart disease; CPET,
CHD, congenital ... heart disease; CPET ... veno-occlusive disease ... bronchopulmonary dysplasia; CLD ... , chronic lung disease