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Cholestatic Liver Disease: Primary Biliary Cirrhosis vs Primary Sclerosing Cholangitis

#pathophysiology #pbc #psc #hepatology #comparison
Disease: Primary Biliary ... Primary Sclerosing Cholangitis ... pathophysiology #pbc ... #psc #hepatology
Summary table of comparison of the difference between primary biliary cholangitis (PBC) and primary sclerosing cholangitis
between primary biliary ... cholangitis (PBC ... primary sclerosing cholangitis ... (PSC).
The 6 C’s of Primary Sclerosing Cholangitis (PSC)
PSC is a chronic, cholestatic, immune-mediated disease characterized by
Primary Sclerosing Cholangitis ... to multi-focal biliary ... • CHOLANGITIS ... colorectal and hepato-biliary ... Primary #Sclerosing #Cholangitis
Classification of Jaundice
Unconjugated hyperbilirubinemia (predominantly indirect bilirubin)
 • Increased bilirubin production (eg, hemolytic anemias, hemolytic reactions,
Dysfunction - Biliary ... certain drugs, biliary ... mononucleosis, cholangitis ... , carcinoma of biliary ... duct, sclerosing cholangitis
Primary Biliary Cirrhosis (PBC) - Summary

PBC Epidemiology:
 • Female:Male 9:1
 • Common European descent
 • Age:
Primary Biliary ... No extrahepatic biliary ... sclerosis group cholangitis ... malignancy #Primary #Biliary ... #cholangitis #diagnosis
Right Upper Quadrant Pain
Liver:
 - Infectious: Acute viral hepatitis, Liver abscess
 - Non-infectious: hepatitis (Alcohol, Medications),
), Budd-Chiari syndrome ... Biliary: - Infectious ... cholecystitis, Acute cholangitis ... "ascending cholangitis ... "biliary colic")
Alkaline Phosphatase (ALP) Elevation - Differential Diagnosis Algorithm

ALP:
 - Enzymes that catalyze hydrolysis of organic phosphate
Drugs - Primary biliary ... Cholangitis (PBC ... Infiltrative diseases - PSC ... - Other biliary
Causes of Biliary Dilatation - Differential Diagnosis
 • Physiological: ↑ Age, Cholecystectomy, Opioid dependence, Post-sphincterotomy
 •
Causes of Biliary ... AUPBD • Stones: Biliary ... sludge), Mirizzi's syndrome ... pancreatitis, PSC ... (or secondary SC
Gallstone Diseases
1. Asymptomatic Stones 75%
2. Biliary Pain 20%
3. Acute Cholecystitis 10%
4. Mirizzi's Syndrome < 0.1%
5. Cholangitis/
Biliary Pain 20% ... Mirizzi's Syndrome ... Cholangitis/ Pancreatitis ... Fistula/Bouveret's Syndrome
Jaundice - Differential Diagnosis Algorithm
Pre-Hepatic - Unconjugated Hyperbilirubinemia
Increased Production
 • Hemolysis
 • Ineffective Erythropoiesis
 • Hematoma
Decreased
• Gilbert's Syndrome ... Crigler-Najjar Syndromes ... on Ultrasound Biliary ... Gallstones • Biliary ... Primary Sclerosing Cholangitis