22 results
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... ANCA-positive vasculitis ... ANCA-negative vasculitis ... erythematosus, Rheumatoid arthritis ... Investigations • Labs: CBC
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
and renal abnormalities ... , obstructive pulmonary ... Presentation - Systemic Symptoms ... Lab Tests: • CBC ... • Urinalysis (Renal
Rheumatoid Arthritis Summary
MCP and PIP Involvement, Spares DIP, Carpal Tunnel, Sicca Syndrome, Epi/Scleritis, Heart Disease, Rheumatoid
Rheumatoid Arthritis ... , Rheumatoid Vasculitis ... Rheumatoid Nodules, Pulmonary ... Disease and ILD ... rheumatology #signs #symptoms
Highlighted Conditions With Arteritis or Periarteritis of the Coronaries
Takayasu's arteritis:
 - Onset < 40 yrs
 -
yrs - Cranial symptoms ... multiplex ANCA vasculitis ... sinusitis - pulmonary ... Leukocytoclastic vasculitis ... Behcet's disease
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
and renal abnormalities ... Presentation: Systemic Symptoms ... GCA (Giant Cell Arteritis ... • Progressive symptoms ... and often causes arthritis
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Pulmonary Renal ... Autoimmune ANCA vasculitis ... life-threatening diseases ... Inflammatory eye disease ... or serologies + symptoms
IgA Vasculitis – Henoch Scholein Purpura: Pathogenesis and Clinical Findings

 - Infectious Agents - 50% have
Intussusception - Renal ... nephritic syndrome, renal ... Arthralgia's (common), arthritis ... HenochScholeinPurpura #Pathophysiology ... Diagnosis #Signs #Symptoms
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Butterfly rash, Vasculitis ... of hip (rare), Arthritis ... Abdominal pain (20%) Renal ... disease (30%): ... erythematosus #signs #symptoms
Rheumatoid arthritis (RA): Extra-articular manifestations
Skin: 
 • Inflammation of skin (esp. over areas of stress) forms
Rheumatoid arthritis ... blood vessels (vasculitis ... interstitial lung disease ... /pulmonary fibrosis ... #signs #symptoms
Rheumatoid Arthritis - Signs and Symptoms
 • Ocular: Keratoconjunctivitis sicca, Episcleritis, Scleritis, Scleromalacia perforans
 • Pulmonary:
Rheumatoid Arthritis ... - Signs and Symptoms ... Scleromalacia perforans • Pulmonary ... Vascular: Rheumatoid vasculitis ... Pericarditis • Renal