17 results
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Clinical Classification ... pulmonary disease ... multifactorial mechanisms Hematologic ... neurofibromatosis, vasculitis ... Hypertension #PHTN #Classification
Chronic Obstructive Pulmonary Disease (COPD)
 • COPD Definition
 • Role of PFTs
 • COPD Classification and
Chronic Obstructive Pulmonary ... Disease (COPD) ... Classification ... #Disease #COPD ... #diagnosis #management
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
progressing GN • New pulmonary ... glomerulonephritis and/or pulmonary ... arthritis, obstructive pulmonary ... differential #diagnosis #rheumatology ... #classification
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Cryoglobulinemia Vasculitis ... - French Vasculitis ... Target plasma cells ... /or refractory disease ... #Management #Rheumatology
Hemolytic Anemia - Differential Diagnosis Algorithm
 • Sickle cells - Consider sickle cell disease (diverse genotypes):
Algorithm • Sickle cells ... Agglutination - Cold ... agglutinins disease ... cardiac valve, vasculitis ... Algorithm #workup #hematology
Cold Agglutinin Disease

3 Types of Cold Sensitive Antibodies:
  1. Cold Agglutinins (CAD)
  2. Donath-Landsteiner
Disease 3 Types ... Cryoglobulins (Vasculitic ... Agglutinin Disease ... sensitize red blood cells ... hemolytic #anemia #hematology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
progressing GN • New pulmonary ... Multinucleated giant cells ... MPO > PR3) • Pulmonary ... Granulomas, IgE, pulmonary ... Differential #Diagnosis #Rheumatology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
when plasma is cooled ... with autoimmune diseases ... malignancies, vasculitis ... thrombophlebitis, pulmonary ... #hematology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... panuveitis, retinal vasculitis ... matter, spinal cord ... Syndrome #diagnosis #management ... signs #symptoms #rheumatology
Kawasaki Disease (KD) - Diagnosis and Management Summary

Kawasaki Disease (KD) is the most common vasculitis of
Kawasaki Disease ... the most common vasculitis ... Erythema of palms or soles ... #KD #vasculitis ... #rheumatology #