50 results
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... destructive sinusitis, pulmonary ... Interstitial lung disease ... Cryoglobulinemic vasculitis ... syndrome • IgA vasculitis
Erythema Annulare Centrifugum (EAC),
This is erythema annulare centrifugum (EAC), one of the “figurate erythemas.” These lesions
Erythema Annulare ... EAC), This is erythema ... the “figurate erythemas ... drugs, systemic disease ... #dermatology #skinrash
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
infection • Lyme disease ... migrans • Lyme disease ... Erythema marginatum ... Hypersensitivity vasculitis ... Antiphospholipid-antibody syndrome • Vasculitis
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... 50% Cutaneous Vasculitis ... Leukocytoclastic Vasculitis ... • Erythema elevatum ... : • Behcet Disease
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
progressing GN • New pulmonary ... glomerulonephritis and/or pulmonary ... arthritis, obstructive pulmonary ... disease, and ocular ... (Granulomatous disease
Erythemas Summarized
Erythema ab igne
 • A dermatosis that results from repeated exposure to heat (fires, heating
Erythema ab igne ... early localized disease ... of necrotizing vasculitis ... called "Bazin's disease ... so-called fifth disease
Pyoderma Gangrenosum: Autoimmune disorder resulting in a vasculitis which causes slowly progressive 
ulceration of the skin.
resulting in a vasculitis ... number of systemic diseases ... inflammatory bowel disease ... suffers from Crohn's Disease ... #Dermatology #SkinRash
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... ANCA-positive vasculitis ... ANCA-negative vasculitis ... IgA-associated vasculitis ... , Behcet disease
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Pulmonary Renal ... ANCA Associated Vasculitis ... - Anti-GBM Disease ... , Behcet's Disease ... Kumfer @AnnKumfer #Pulmonary
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
due to lung disease ... lung disease Other ... pulmonary disease ... neurofibromatosis, vasculitis ... , Gaucher disease