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Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... 50% Cutaneous Vasculitis ... Secondary: CTD: SLE, RA ... related vasculitis ... • Erythema elevatum
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
Dermatomyositis Erythema ... Lyme disease Erythema ... Hypersensitivity vasculitis ... gangrenosum • IBD • RA ... Antiphospholipid-antibody syndrome • Vasculitis
Rheumatoid Arthritis Summary
MCP and PIP Involvement, Spares DIP, Carpal Tunnel, Sicca Syndrome, Epi/Scleritis, Heart Disease, Rheumatoid
Disease, Rheumatoid Vasculitis ... Rheumatoid Nodules, Pulmonary ... Felty's Syndrome (RA ... Rheumatoid #Arthritis #RA
ILD of Known Cause - Differential Diagnosis
Exposure:
 • Occupational: Asbestosis, Silicosis, Hypersensitivity, Pneumonitis
 • Treatment Related:
Granulomatous DX with Vasculitis ... Tissue Disease: RA ... lung #disease #pulmonary
Non-Resolving Pneumonias: Etiologies
Unusual Infections:
 - Immunocompromised patients (e.g.: Mycobacterium, Aspergillosis, Nocardia)
 - Endemic Fungi (e.g.: Histoplasmosis,
disorders: - Vasculitis ... - Other Rheum (RA ... Others: - Pulmonary ... abnormalities (Pulmonary ... Pneumonia #diagnosis #pulmonary
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
• Scleritis - RA ... Nodules • RA ... Wilson's disease Pulmonary ... Spondyloarthropathies, SLE • Pulmonary ... Lyme disease, Vasculitis
Rheumatoid arthritis (RA): Extra-articular manifestations
Skin: 
 • Inflammation of skin (esp. over areas of stress) forms
Rheumatoid arthritis (RA ... blood vessels (vasculitis ... effusion on CXR • RA ... interstitial lung disease/pulmonary ... RheumatoidArthritis #RA
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... Painful or pruritic erythema ... thrombophlebitis, pulmonary
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
overlaps with RA ... Disease: • 10%-15% Pulmonary ... , INC risk PE, Pulmonary ... ) • Cutaneous vasculitis ... : 2% Systemic Vasculitis
RHEUMATOID LUNG DISEASE:
•	RA-associated interstitial lung disease (RA-ILD).
•	Pleural disease (pleural thickening/effusions).
•	Airway disease (Both upper & lower airway).
•	Rheumatoid
LUNG DISEASE: • RA-associated ... lung disease (RA-ILD ... thromboembolic disease • Vasculitis ... Pulmonary function ... #ILD #RA #Rheumatoidlungdisease