6 results
The idiopathic interstitial pneumonias (IIPs) comprise a heterogenous group of disorders. 
They represent fundamental responses of
The idiopathic interstitial ... combinations of fibrosis ... Diagnosis #Radiology #Pulmonary ... #CTChest #Idiopathic ... IdiopathicInterstitialPneumonia #ILD
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
Multi-system autoimmune disease ... and progressive fibrosis ... skin thickening Signs ... : ILD (interstitial ... lung disease),
Rheumatoid arthritis (RA): Extra-articular manifestations
Skin: 
 • Inflammation of skin (esp. over areas of stress) forms
pleural effusion on CXR ... tends to cause interstitial ... lung disease/pulmonary ... fibrosis (mechanism ... #signs #symptoms
Bronchiectasis - Summary

What?
• Bronchiectasis is derived from the Greek words bronckos meaning airway and ectasis meaning
Causes: • Cystic fibrosis ... Connective tissue diseases ... evidence of cystic fibrosis ... Nasal polyps and signs ... disease Complications
Sarcoidosis - Diagnosis and Management Summary
Epidemiology
1) High incidence in Scandinavian countries (11-24 cases per 100,000 individuals
survival is 93-95% Pathophysiology ... fibroblasts → fibrosis ... e.g. incidental CXR ... Pulmonary: dyspnea ... Diagnosis #Management #Signs
Ankylosing Spondylitis: Extra-articular Manifestations
 • Ocular - Inflammation of the iris, the anterior part of the
Inflammatory Bowel Disease ... (IBO), but IBD ... -> Apical lung fibrosis ... Complications #pathophysiology ... #diagnosis #signs