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Myasthenia Gravis Overview

Myasthenia Gravis is an autoimmune disorder of the postsynaptic neuromuscular junction.  Ab to
Myasthenia Gravis ... Serologic and EMG ... Gravis Treatment ... - Symptomatic Treatment ... #management #neurology
Myasthenia Gravis - Summary
 • an autoimmune disease of the postsynaptic neuromuscular junction associated with antibodies
Myasthenia Gravis ... serologic, and EMG ... characteristic EMG ... #Gravis #diagnosis ... #management #neurology
Causes of Neuromuscular Weakness
 • Spinal Cord: Demyelinating Disease (MS), Epidural abscess, Infarction, Syringomyelia, Tetanus, Transverse
Poliomyelitis, Guillain-Barre ... Eaton Syndrome, Myasthenia ... Gravis, Organophosphate ... differential #diagnosis #neurology
Causes of Fatigue - Differential Diagnosis Algorithm
Endocrine
 • Hypo/Hyperthyroidism
 • Diabetes
 • Pituitary Insufficiency
 • Adrenal
Pulmonary Disease Neurologic ... Parkinson's • Myasthenia ... Gravis Pharmacologic ... • Drug Abuse (e.g
Guillain-Barre Syndrome - Summary

Acute AIDP that presents with rapidly progressive flaccid weakness

Epidemiology:
 • 1-2 cases/100,000 per
Guillain-Barre Syndrome ... Electrodiagnostic studies - EMG ... Treatment: • Plasmapheresis ... diagnosis #management #treatment ... #neurology
Neuromyelitis Optica (NMO) - Clinical Manifestations
 • Optic neuritis: Reduced visual acuity, ranging from mild to
brainstem syndromes (e.g ... AQP4-lgG disease; e.g ... Sjögren syndrome, Myasthenia ... gravis, Many others ... Manifestations #diagnosis #neurology
Weakness - Differential Diagnosis Framework

Approach To Weakness:
 • Non-neuromuscular disorder (Cardiac, pulmonary etc)
 • CNS ->
Postsynaptic: Myasthenia ... Gravis - Lack ... aminotransferases • Serology ... electromyographic (EMG ... Differential #Diagnosis #neurology
Statin Induced Muscle Toxicity - Summary

Clinical Presentation:
 • Elevations of serum creatine kinase with proximal myalgia
any time during treatment ... hypothyroid-induced myopathy, Guillain-Barré ... Lambert-Eaton myasthenic ... (SAMS-CI) • EMG ... after DC Statin Treatment
Guillain-Barré Syndrome (GBS)
Acute autoimmune demyelinating polyradiculoneuropathy that presents with rapidly progressive flaccid weakness
Epidemiology:
 • Incidence: 1
Guillain-Barré Syndrome ... Electrodiagnostic studies (Ex EMG ... and cauda equina TREATMENT ... SinaiBmoreIMRes #GBS #Guillain ... diagnosis #management #neurology