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A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
#Diagnosis # ... #Small #Medium ... Large #Vessel #Size ... #Classification ... #Differential #Algorithm
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
based on vessel size ... small vessel vasculitis ... can affect any type ... #Diagnosis #Rheumatology ... #Classification
Break down Vasculitis based on vessel size
#Diagnosis #Rheumatology #Differential #Vasculitis #VesselSize #Small #Medium #Large #Classification
based on vessel size ... #Diagnosis #Rheumatology ... #VesselSize #Small ... #Medium #Large ... #Classification
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
abnormalities SMALL ... + MPO-ANCA MEDIUM ... Findings by Vessel Size ... against MPO • Complement ... #rheumatology #classification
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... of medium vessels ... of small vessels ... dermatomyositis #Size ... #Diagnosis
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Labs/Diagnosis: ... • Low serum C4 complement ... • Cutaneous small-vessel ... Cryoglobulins #diagnosis ... #types #classification
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
, fibronectin, small ... Divided Into Two Types ... malignancies, vasculitis ... : Occlusion of small ... to medium-sized
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
anti-Smith Ab, low complements ... Skin Disease Classification ... Differential Diagnosis ... Kikuchi disease • Type-I ... inflammation of the small
Monoclonal Gammopathy of Renal Significance (MGRS)

MGRS
• MGRS refers to kidney disease caused by nephrotoxic monoclonal immunoglobulins
Immunofixation (SIFE ... guide subtype classification ... tubulopathy) - Complement ... formation causing vasculitis ... Types of MGRS-Associated