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A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
#Diagnosis # ... #Small #Medium ... #Large #Vessel # ... Size #Classification ... #Differential #Algorithm
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
based on vessel size ... Large vessel vasculitis ... can affect any type ... #Diagnosis #Rheumatology ... #Classification
Break down Vasculitis based on vessel size
#Diagnosis #Rheumatology #Differential #Vasculitis #VesselSize #Small #Medium #Large #Classification
based on vessel size ... #Diagnosis #Rheumatology ... #VesselSize #Small ... #Medium #Large ... #Classification
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
abnormalities SMALL ... Findings by Vessel Size ... : • Large Vessel ... against MPO • Complement ... #rheumatology #classification
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... of large vessels ... of small vessels ... dermatomyositis #Size ... #Diagnosis
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Labs/Diagnosis: ... • Low serum C4 complement ... • Cutaneous small-vessel ... Cryoglobulins #diagnosis ... #types #classification
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
anti-Smith Ab, low complements ... Skin Disease Classification ... Kikuchi disease • Type-I ... inflammation of the small ... and large bowel
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
Cytopenia: 2% • Hypocomplementemia ... nervous system: small-fiber ... ) • Cutaneous vasculitis ... : 2% Systemic Vasculitis ... cell lymphoma • Large
Monoclonal Gammopathy of Renal Significance (MGRS)

MGRS
• MGRS refers to kidney disease caused by nephrotoxic monoclonal immunoglobulins
Immunofixation (SIFE ... guide subtype classification ... tubulopathy) - Complement ... formation causing vasculitis ... Types of MGRS-Associated