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A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
A System for Vasculitides ... Diagnosis #IM #Rheum #Vasculitis ... #Small #Medium ... #Vessel #Size #Classification ... #Differential #Algorithm
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
, medium vessel ... small vessel vasculitis ... Medium vessel vasculitis ... Small vessel vasculitis ... #Classification
Break down Vasculitis based on vessel size
#Diagnosis #Rheumatology #Differential #Vasculitis #VesselSize #Small #Medium #Large #Classification
Break down Vasculitis ... #Differential #Vasculitis ... #VesselSize #Small ... #Medium #Large ... #Classification
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
abnormalities SMALL ... + MPO-ANCA MEDIUM ... against MPO • Complement ... , and SLE) • Urinalysis ... #rheumatology #classification
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Secondary: CTD: SLE ... Findings: • Small ... Urticaria • Medium ... ulceration Small ... elevatum diutinum Medium
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
semiology of Cutaneous Vasculitis ... involvement of small ... wall vessels (medium-sized ... disease (10%) : SLE ... +++ • IgA vasculitis
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... Vasculitis Vasculitis ... of medium vessels ... of small vessels ... dermatomyositis #Size #Classification
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
diseases: - 10% SLE ... • Low serum C4 complement ... • Cutaneous small-vessel ... erythematosus (SLE ... diagnosis #types #classification
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
diseases, such as SLE ... primary condition MEDIUM ... and infarcts SMALL ... Elevated AST ALT • Hypocomplementemia ... ) • Hypocomplementemic
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
multiple organs, small-vessel ... Arterial (MCC-small ... Medium and large ... Oral aphthae : SLE ... • Arthritis: SLE