11 results
Causes of Hypocomplementemia - CHAMPS Mnemonic
C - Cryoglobulinemia (85%), C3 glomerulopathy, cirrhosis
H - Heavy Chain deposition
Causes of Hypocomplementemia ... Chain deposition disease ... @AnnKumfer #Hypocomplementemia ... #Low #Complement ... #diagnosis #differential
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential Diagnosis ... often involved • Hypocomplementemic ... Urticaria and hypocomplementemia ... Differential Diagnosis ... against MPO • Complement
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... PET-CT Imaging (→ Diagnostic ... rheumatoid factor), ± hypocomplementemia ... IgG4 #Related #Disease ... #diagnosis #management
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
staining): • Low Complement ... Idiopathic • Normal Complement ... involvement: Anti-GBM Disease ... #differential #diagnosis ... #algorithm #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
- Differential Diagnosis ... Vasculitis Differential Diagnosis ... Elevated AST ALT • Hypocomplementemia ... Vasculitis) • Hypocomplementemic ... #Differential #Diagnosis
Recommended initial testing for patients being evaluated for glomerular disease 

24-hour urine collection - Quantify proteinuria.
for glomerular disease ... SPEP+free light chains ... or alternative complement ... of glomerular disease ... testing #workup #diagnosis
Recommended initial testing for patients being evaluated for glomerular disease
1) 24-hour urine collection - Quantify proteinuria.
for glomerular disease ... or alternative complement ... SPEP+free light chains ... #glomerular #disease ... #workup #diagnosis
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
multisystemic disease ... Sjogren's Syndrome Diagnosis ... Cytopenia: 2% • Hypocomplementemia ... RTA, TYPE I RTA Diagnosis ... #Rheumatology #Diagnosis
HSCT related renal disease - AKI and CKD
Acute Kidney Injury: Acute GvHD 2-4, Pre renal state,
related renal disease ... Veno occlusive disease ... body irradiation, Complement ... #differential #diagnosis ... #algorithm
Causes of Hyperkinetic Movement Disorders - Differential Diagnosis Algorithm
Tics:
 • Tourette's Syndrome
 • Attention Deficit Hyperactivity
- Differential Diagnosis ... Algorithm Tics ... dystonia • Writer's cramp ... • Huntington's Disease ... #Algorithm #Causes