9 results
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
: Overwhelming clinical ... syndrome associated ... age, however the disease ... lymph node, or liver ... #hematology
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Clinical Presentation ... Fever is the main clinical ... thrombocytopenia • Liver ... Treatment: • Corticosteroids ... Diagnosis #Management #Hematology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
common in Asia • HLA-B51 ... association • M > F Clinical ... (Clinical Dx). ... Arthritis, AS Treatment ... signs #symptoms #rheumatology
Hepatopulmonary Syndrome - Diagnosis and Management Summary
A defect in arterial oxygenation due to a gas exchange
Hepatopulmonary Syndrome ... shunt (Type 2) Clinical ... ) on room air Treatment ... hepatopulmonary #syndrome ... #hepatology
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
Sjogren's Syndrome ... salivary ducts Clinical ... vasculitis: 10%-16% Liver ... Nephrogenic DI Hematologic ... Adenocarcinoma Treatment
Hepatopulmonary Syndrome - Illness Script
HPS is a pulmonary disorder of chronic liver disease characterized by a
Hepatopulmonary Syndrome ... of orthodeoxia CLINICAL ... the left heart TREATMENT ... only definitive treatment ... cirrhosis #diagnosis #hepatology
Retinoblastoma - MRI
 • Most common intra-ocular neoplasm in children.
 • Clinical Presentation: leukocoria (loss of
Clinical Presentation ... Leptomeningeal disease ... bone marrow and liver ... neuroradiology #pediatrics ... #radiology
Iliotibial Band Friction Syndrome - MSK Radiology
Imaging Findings:
 • The iliotibial band (ITB) is thickened with
Band Friction Syndrome ... - MSK Radiology ... • Treatment: Conservative ... Findings of chronic disease ... #Radiology #diagnosis
Double Shunt on Echocardiogram
What do you see on this saline contrast study, in a patient with
with end-stage liver ... disease and pulmonary ... hepatopulmonary syndrome ... Echocardiogram #clinical ... intrapulmonary #cardiology