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Congenital Heart Disorders - Classification and Differential Algorithm

- Amy Chung, MD, MSc @AmyChung 

#Congenital #Heart #Disorders
Heart #Disorders #Diseases ... #Classification ... Diagnosis #Peds #Pediatrics ... #Cardiology #Cyanotic ... #Pink #Blue
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Clinical Classification ... - HIV infection ... pulmonary disease ... , Gaucher disease ... Hypertension #PHTN #Classification
Undifferentiated critical congenital heart disease: Patterns of Presentation 
Pink baby:
 • Presents at 1-6 mo
Undifferentiated critical ... congenital heart disease ... if cardiac or pulmonary ... screens catch blue ... Gray #Baby #Peds #Pediatrics
Tetralogy of Falot on Chest X-Ray
Tetralogy of Falot comprises four defects -
1. Ventricular septal defect (VSD)
2.
along with concave Pulmonary ... Cyanotc Heart Diseases ... Chest #XRay #CXR #clinical ... #radiology #peds ... #pediatrics #cardiology
Nontuberculous mycobacteria
Nontuberculous mycobacteria, also known as atypical mycobacteria, are all the other mycobacteria which can cause
which can cause pulmonary ... disease resembling ... patient with active disease ... upper lobes due to infection ... #Clinical #Radiology
There is a hydropneumothorax.
Notice the air-fluid level (blue arrow).
The upper lobe is still attached to the
air-fluid level (blue ... a cystic lung disease ... is a rare lung disease ... airways leading to pulmonary ... #Clinical #Radiology
Progressive Massive Fibrosis aka Complicated Silicosis.
Silicosis is a fibrotic lung disease caused by inhalation of crystalline
fibrotic lung disease ... With disease progression ... Fibrosis #Silicosis #clinical ... #radiology #CXR ... XRay #labeled #pulmonary
Miliary Pattern - Chest Radiology
 • Miliary opacities are scattered, small (1 -4 mm) nodules
 •
Pattern - Chest Radiology ... hematogenous spread of a disease ... Sarcoidosis, HSP • Inhalation ... differential #diagnosis #pulmonary ... #CXR #clinical
Preoperative Risk Evaluation

Major Pre-Op Questions:
1. Does the patient have any modifiable risk factors that could be
murmur 3/6) - Pulmonary ... Skin exam for infection ... Change in clinical ... days before Pulmonary ... one post op Cardiology
Pulmonary sequestration
This is an uncommon cause of lobar consolidation.
It is a congenital abnormality.
A nonfunctioning part of
Pulmonary sequestration ... with recurrent infection ... from the aorta (blue ... #Clinical #Radiology ... #CXR #CtChest #Pulmonary