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Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
I-JIP: usual interstitial ... AIP: acute interstitial ... ConnectiveTissueDiseases #ILD ... #Comparison #Table ... #Pulmonary #Rheumatology
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
• Idiopathic pulmonary ... pneumonia (DIP) ... pneumonia (AIP) ... #diagnosis #differential ... #pulmonary #causes
Causes of Interstitial Lung Disease - Differential Diagnosis Algorithm
Idiopathic Interstitial Pneumonia
 • (UIP) Usual Interstitial Pneumonia
Lung Disease - Differential ... Pneumonia • (UIP ... leaking out of pulmonary ... Lung #Diseases #ILD ... #Causes #Differential
Upper lung zone preference is seen in:
- Inhaled particles: pneumoconiosis (silica or coal)
- Smoking related diseases
bronchiolitis (RB-ILD ... is seen in: - UIP ... edema #Diagnosis #Radiology ... #Pulmonary #HRCT ... #ChestCT #Differential
Here are the most common examples of these four patterns on a chest x-ray (click image
consolidation - Multifocal ill-defined ... - Reticular interstitial ... mass - Solitary Pulmonary ... Atelectasis #Diagnosis #Clinical ... #Radiology #CXR
Ground-glass opacity
Ground-glass opacity (GGO) represents:
- Filling of the alveolar spaces with pus, edema, hemorrhage, inflammation or
Thickening of the interstitium ... predominance: UIP ... bronchiolitis #Diagnosis #Radiology ... #Pulmonary #CTChest ... #GroundGlass #Differential
The idiopathic interstitial pneumonias (IIPs) comprise a heterogenous group of disorders. 
They represent fundamental responses of
The idiopathic interstitial ... findings of NSIP, UIP ... #Diagnosis #Radiology ... #Pulmonary #CTChest ... IdiopathicInterstitialPneumonia #ILD
Typical UIP with honeycombing and traction bronchiectasis in a patient with idiopathic pulmonary fibrosis (IPF) #Clinical
Typical UIP with ... with idiopathic pulmonary ... fibrosis (IPF) #Clinical ... #Radiology #CTChest ... #UIP #IPF #ILD
Differential diagnosis on HRCT
Most of our knowledge about imaging findings in interstitial lung disease comes from
Differential diagnosis ... in many cases UIP ... #Diagnosis #Radiology ... #Pulmonary #CXR ... Pattern #Differential
HRCT findings in UIP
Honeycombing consisting of multilayered thick-walled cysts.
Architectural distortion with traction bronchiectasis due to fibrosis.
Predominance
HRCT findings in UIP ... lymphadenopathy #Clinical ... #Radiology #CTChest ... #Usual #Interstitial ... #Pneumonitis #ILD