2 results
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
infection risk secondary ... disease • Liver ... diseases and hepatitis ... hemolytic anemia) • Systemic ... DDX - Other causes
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
hyperinflammatory syndrome caused ... of the immune system ... STX11, STXBP2 • Secondary ... - Elevated liver ... Diagnosis #Management #Hematology