15 results
BEE Syndromes - Immune-mediated conditions affecting the brain, eye, and ear

Visual or auditory symptoms in conjunction
BEE Syndromes - ... treatment can prevent ... Inflammatory causes ... polychondritis • Behcet ... #Syndromes #neurology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behçet's Syndrome ... in Behcet syndrome ... adenopathy (PFAPA) syndrome ... #Syndrome #diagnosis ... #symptoms #rheumatology
BEE Syndromes - Non-inflammatory Causes

Immune-mediated conditions affecting the Brain, Eye, and Ear

Visual or auditory symptoms in
BEE Syndromes - ... treatment can prevent ... recessive—Usher syndrome ... • Other • Syndromes ... #Syndromes #neurology
Myasthenia Gravis Overview

Myasthenia Gravis is an autoimmune disorder of the postsynaptic neuromuscular junction.  Ab to
thyroid, Sjogren syndrome ... “dropping head syndrome ... - Kearns-Sayre syndrome ... Eaton myasthenia syndrome ... #neurology
Cauda Equina Syndrome Overview

Cauda Equina Syndrome:
 • Prevalence: 1:33,000-100,000 ppl/yr
 • Incidence: 1.5-3.4 million ppl/yr
 •
Cauda Equina Syndrome ... Cauda Equina Syndrome ... - Cauda equina syndrome ... of Cauda Equina Syndrome ... Guillain-Barre syndrome
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Mucocutaneous lymph node syndrome ... often causes arthritis ... vasculitis • Behcet ... syndrome: Recurrent ... vasculitis • Cogan syndrome
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
SAPHO Syndrome Summary ... SAPHO syndrome is ... glucocorticoid • SAPHO syndrome ... retinoid • SAPHO syndrome ... #SAPHO #Syndrome
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
often causes arthritis ... Mucocutaneous lymph node syndrome ... VASCULITIS: • Behçet ... Syndrome: - Recurrent ... • Cogan Syndrome
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
common systemic inflammatory ... with systemic, neurologic ... variably: On one hand ... the “Chewing gum test ... #Diagnosis #Management
Hypertrophic Pachymeningitis - Differential Diagnosis Framework

Pachymeningitis is a rare condition that causes areas of a layer
different symptoms ... • Rheumatoid arthritis ... polychondritis • Behçet ... brain sagging syndrome ... type 4: distal nerve