10 results
X-Linked Agammaglobulinemia: Pathogenesis and clinical findings
The epidemiology of this disease is 1/340,000 births and roughly double
Pathogenesis and clinical ... epidemiology of this disease ... history of the disease ... > Inability to produce ... infections (e.g
Blood Product Transfusions One Pager Summary
Type and screen - determines blood type and detects in recipient
in recipient (e.g ... very rare), or bacterial ... - Bacterial ... RBCs (stored at 4C ... diagnosis #management #hematology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
of fibrin split products ... • Fibrin split products ... Cryofibrinogenemia Clinical ... Diagnosis: • + Clinical ... Atherosclerotic PVD
Blood Transfusion Reactions

Immune Mediated:
 • Febrile Non-Hemolytic Transfusion Reaction (FNHTR): Most common immune reaction to transfusion.
FNHTR once had ... very rare), or bacterial ... • Bacterial contamination ... RBCs (stored at 4C ... diagnosis #management #hematology
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
fever syndromes Clinical ... Fever is the main clinical ... Fibrin degradation products ... Treatment: • Corticosteroids ... #Rheumatology
Spontaneous Bacterial Peritonitis
DIAGNOSTICS
Paracentesis: 
 • Calculate absolute PMN count (total WBC x PMN %)
 • Correct
Treat if other signs ... 1: 1.5 g/kg of ... ↓ rebleeding, infections ... advanced liver disease ... #prophylaxis #treatment
Peripartum Cardiomyopathy - Summary
1. Definition
 • Towards the end of pregnancy to 5 months postpartum
Clinical • Under-recognized ... exertion, orthopnea, PND ... Avoid estrogen products ... diagnosis #management #cardiology ... #treatment
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
HLH is a critical ... ▪ Autoimmune diseases ... Clinical Presentation ... • Common Signs ... Diagnosis #Management #Hematology
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
chest (in a V-sign ... auricular papules Clinical ... more severe disease ... positive patients Treatment ... diagnosis #management #rheumatology
Cryptococcal meningitis on T2 MRI
30 M from sub-Saharan Africa presents w/ progressive Headache x1 mo, +neck
gelatinous cyst produced ... organism (soap bubble sign ... Standard treatment ... University Infectious Diseases ... T2 #MRI #Brain #clinical