6 results
Hypereosinophilia Syndrome (HES) - Diagnosis and Management
Definition: An absolute eosinophil count (AEC) greater than 1500 and
Diagnosis and Management ... Secondary Causes ... #diagnosis #hematology ... #differential # ... management #eosinophils
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
Retroperitoneum and aorta ... conventional imaging (aorta ... phase reactants, eosinophilia ... Disease #diagnosis #management ... workup #treatment #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
• EGPA: - Eosinophilia ... tract, and often causes ... < 30 years - Aorta ... and branches • GCA ... : - Aorta and
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
those coming off aorta ... very remarkable w/differential ... identifies 85 to 95% of cases ... them, but urgent rheumatology ... Symptoms #Diagnosis #Management
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
< 30 years • Aorta ... Arteritis): • Aorta ... Polyangiitis): • Eosinophilia ... tract, and often causes ... #Diagnosis #Rheumatology
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
Large vessels (aorta ... Polyarteritis Nodosa, GCA ... Loss of vision • Aortic ... Polychondritis #rheumatology ... #diagnosis #management