9 results
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... biliary, renal, lung ... concentration PET-CT ... #diagnosis #management ... workup #treatment #rheumatology
Lung Abscess - Diagnosis and Management Summary

Lung Abscess Etiology:
 • Necrosis of lung parenchyma by a
Lung Abscess - Diagnosis ... Lung abscess ... anemia • Sputum/Blood ... seen • Chest CT ... Lung Abscess
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
• Chronic lung ... lymphocytic interstitial lung ... Chest CT: • Ground-glass ... : • Low serum IgG ... trough levels of IgG
Endocarditis Summary

Who?
Infectious:
• Pre-existing valvular disease
• Prosthetic valve
• Congenital heart disease
• IV substance use
• IV catheter
• Recent
verrucous) • Lung ... , Pancreas, Gastric ... Microbiology: Blood ... • Blood cultures ... Endocarditis #diagnosis #management
Blood Product Transfusions One Pager Summary
Type and screen - determines blood type and detects in recipient
Blood Product Transfusions ... Related Acute Lung ... Blood products contain ... #diagnosis #management ... #hematology #reactions
Blood Transfusion Reactions

Immune Mediated:
 • Febrile Non-Hemolytic Transfusion Reaction (FNHTR): Most common immune reaction to transfusion.
Related Acute Lung ... Blood products contain ... of transfused products ... #diagnosis #management ... #hematology #reactions
Scleroderma Like Conditions - Differential Diagnosis
Eosinophilic Fasciitis:
 - Orange peel induration (peau d'orange) of proximal extremities
Typically seen in long-standing ... paraproteinemia (IgGλ ... be seen after blood ... Exposure: - Can produce ... Differential #Diagnosis #comparison
Mycoses

HISTOPLASMOSIS
• Inhalation of conidia → Yeast → travel to lymph nodes → spread in body
• Bird
pulmonary symptoms • Rheumatologic ... dissemination occurs and produces ... Sinusitis • Brain abscess ... change in the lungs ... Fungal #Diagnosis #Management
Langerhans Cell Histiocytosis (LCH)

Granulomatous Lesions comprising langerin-positive histiocytes and an inflammatory infiltrate can arise in virtually
Imaging: X-rays, CT ... PET-CT / MRI: Staging ... Laboratory Tests: Blood ... tests to assess ... Histiocytosis #Diagnosis #Management