81 results
Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
Connective tissue disease-associated ... interstitial lung ... diseases LIP ... PSS: Sjogren syndrome ... connective tissue disease
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
Diseases (ILD) ... Connective Tissue Disease ... connective tissue disease ... disease (RB-ILD ... #Diseases #ILD
Nail Clubbing - Differential Diagnosis Algorithm
Bronchopulmonary Disease
 • Bronchiectasis
 • Chronic Lung Infection
 • Lung Cancer
- Differential Diagnosis ... Bronchiectasis • Chronic Lung ... Infection • Lung ... Immunodeficiency Virus ... #Differential #Diagnosis
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... biliary, renal, lung ... concentration PET-CT ... IgG4 #Related #Disease ... #diagnosis #management
Hepatopulmonary Syndrome (HPS) 

HPS-differential diagnosis:
1. Pulmonary vasculature
2. Diseases of the lung parenchyma
3. Pleura and diaphragm

HPS-diagnosis:
1. Patients
Hepatopulmonary Syndrome ... Diseases of the ... lung parenchyma ... Patients with liver disease ... #HPS #hepatology
Causes of Pulmonary Hypertension - Differential Diagnosis Algorithm
Pulmonary Arterial Hypertension
 • Idiopathic
 • Associated with:
Connective Tissue Disease ... Congenital Heart Disease ... Dysfunction: • Systolic ... Disease and/or ... Thromboembolic Disease
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Systolic dysfunction ... hypertension due to lung ... Interstitial lung ... multifactorial mechanisms Hematologic ... Classification #Diagnosis
Pancytopenia - Differential Diagnosis

Congenital Diseases:
• GATA2 deficiency
• Fanconi’s anemia
• Wiskott-Aldrich syndrome
• Ribosomopathy or telomeropathy

Cancer:
• Leukemia
• Lymphoma

Inflammatory
Congenital Diseases ... Wiskott-Aldrich syndrome ... and Autoimmune Diseases ... : • Systemic lupus ... #Hematology
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
disease • ... Granulomatous disease ... • Liver diseases ... disease (GLILD) ... #diagnosis #management
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
highly inflammatory disease ... Adult-onset Still disease ... erythematosus • Kawasaki disease ... of underlying disease ... #Diagnosis #Management