7 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
vasculitis) • Cutaneous ... matter, spinal cord ... syndrome (Clinical ... disease) Differential ... : monoclonal TNF-aIpha
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
Identification of causes ... EGPA • Solid cancers ... Vasculitis #dermpath #dermatology ... #diagnosis #clinical ... #lesions #differential
Cold Agglutinin Disease

3 Types of Cold Sensitive Antibodies:
  1. Cold Agglutinins (CAD)
  2. Donath-Landsteiner
Cryoglobulins (Vasculitic ... Viral Infection Clinical ... anemiaCold ... Diagnosis Monoclonal ... #hematology #diagnosis
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
sensitivity • Painful ulcers ... : • + Clinical ... • Negative causes ... Biopsy: Typical pathologic ... hematology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
lesions • Mononeuritis ... tract, and often causes ... VASCULITIS: • Behçet ... Serologies for Cryoglobulins ... #diagnosis #rheumatology
Cutaneous Mucormycosis Eschar
30 M HIV cd4 10 VL 30k traumatic injury of arm few months ago
Diagnosis? ... as non healing ulcer ... trauma, aplastic anemia ... Mucormycosis #Eschar #dermatology ... #skin #clinical
Nontuberculous Mycobacteria (NTM) Infections 

Mycobacterial species other than those belonging to the Mycobacterium tuberculosis complex and
status NTM Cause ... Nodular or cavitary lesions ... , alcohol, cancer ... Hematologic malignancy ... Bone Marrow - Anemia