7 results
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
sensitivity • Painful ulcers ... • Negative causes ... Biopsy: Typical pathologic ... #diagnosis #rheumatology ... #hematology
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
• They can cause ... ulcers - Glomerulonephritis ... Syndrome: • Clinical ... Henoch-Schönlein purpura) • Cutaneous ... #classification
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
Identification of causes ... EGPA • Solid cancers ... Vasculitis #dermpath #dermatology ... #diagnosis #clinical ... #lesions #differential
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... vasculitis) • Cutaneous ... matter, spinal cord ... Behcet disease) Differential ... refractory disease : monoclonal
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
lesions • Mononeuritis ... tract, and often causes ... Serologies for Cryoglobulins ... #diagnosis #rheumatology ... #classification
Cutaneous Mucormycosis Eschar
30 M HIV cd4 10 VL 30k traumatic injury of arm few months ago
Diagnosis? ... as non healing ulcer ... of lesion to subcutaneous ... Mucormycosis #Eschar #dermatology ... #skin #clinical
Nontuberculous Mycobacteria (NTM) Infections 

Mycobacterial species other than those belonging to the Mycobacterium tuberculosis complex and
status NTM Cause ... Nodular or cavitary lesions ... disease, alcohol, cancer ... Hematologic malignancy ... NTM #Infections #differential