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2021 ACR/VF Guidelines for Management of Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA)

#Granulomatosis #Polyangiitis #GPA
2021 ACR/VF Guidelines ... Polyangiitis (GPA ... #Polyangiitis #GPA ... #rheumatology #algorithm ... #vasculitis
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
- ACR/VF 2021 Guidelines ... Polyangiitis (GPA ... ), Microscopic Polyangiitis ... (MPA) • Eosinophilic ... ACR2021 #Guidelines #algorithm
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
>>> MPA > eGPA ... ): eGPA, MPA >>> ... Glomerulonephritis #Vasculitis ... #differential # ... diagnosis #algorithm
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (GPA ... ) and Microscopic ... - ACR/VF 2021 Guidelines ... #Polyangiitis #GPA ... #MPA #ANCA #Vasculitis
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated Vasculitis ... inflammation: • Microscopic ... polyangiitis (GPA ... #differential # ... diagnosis #algorithm
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
the Skin - Differential ... Associated: - Microscopic ... polyangiitis - EGPA ... - GPA Cutaneous ... #rheumatology #differential
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
PR3-ANCA): • Microscopic ... capillaritis • EGPA ... > PR3 60% • GPA ... • ANCA (Dx: GPA ... , EGPA, microscopic
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Autoimmune ANCA vasculitis ... (AAV): GPA (granulomatous ... polyangiitis), MPA ... (microscopic polyangiitis ... subglottic stenosis) in GPA
Mesenteric Ischemia - Differential Diagnostic Schema
Chronic: ASCVD, Venous, Vasculitides 5% (PAN, [E]GPA, IgA, MPA)
Acute
 - Venous
Mesenteric Ischemia - Differential ... ASCVD, Venous, Vasculitides ... 5% (PAN, [E]GPA ... , IgA, MPA) Acute ... #Diagnosis #algorithm
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
Polyangiitis (GPA ... polyangiitis (GPA ... GPA causes disease ... polyangiitis • EGPA ... #Polyangiitis #GPA