986 results
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
Sjogren's Syndrome ... SLE • Mikulicz syndrome ... salivary ducts Clinical ... • Interstitial Pneumonitis ... Rheumatology #Diagnosis #Management
Cystic Lung Disease
Upper Lobe Predominant: 
Langerhans Cell Histiocytosis, Pneumocystis Jiroveci, Hypersensitivity Pneumonitis, Neurofibromatosis Type 1, Paracoccidioidomycosis,
Hypersensitivity Pneumonitis ... Ehlers-danlos Syndrome ... Amyloidosis, Proteus Syndrome ... Birt-Hogg-Dubé Syndrome ... Lymphocytic Interstitial Pneumonitis
Immune Reconstitution Inflammatory Syndrome - Overview of IRIS

What Is IRIS?
	• A state of hyperinflammatory response that
Reconstitution Inflammatory Syndrome ... noncompliance • Clinical ... initiation Clinical ... #Inflammatory #Syndrome ... Differential #Diagnosis #Management
Pulmonary complications of targeted therapy
-Immune checkpoint inhibitors (e.g. pembrolizumab)
-Pneumonitis is uncommon (~5% of patients) but can
pembrolizumab) -Pneumonitis ... well as radiation pneumonitis ... associated with a clinical ... diagnosis pneumonitis ... #Clinical #Diagnosis
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
Hypersensitivity pneumonitis ... • Radiation pneumonitis ... Idiopathic Interstitial Pneumonias ... Churg Strauss syndrome
Inherited Colorectal Cancer (CRS) Syndromes
Adenomatous Polyposis Syndromes:
 • Familial Adenomatous Polyposis (FAP), Attenuated FAP (AFAP), MUTYH
Colorectal Cancer (CRS) Syndromes ... Adenomatous Polyposis Syndromes ... Urinary → Lynch Syndrome ... Peutz-Jeghers Syndrome ... #diagnosis #management
Hemoptysis - Differential Diagnosis Framework
Airways: 
 • Bronchitis
 • Bronchiectasis
 • Malignancy: Primary bronchogenic CA, Endobronchial
Goodpastures, Lupus Pneumonitis ... , GPA, Behcet syndrome ... Osler-Weber-Rendu syndrome
Pulmonary Complications Following Stem Cell Transplant

For patients in the pre- engraftment period (day 0-30):
 - 
Pulmonary
- Engraftment syndrome ... Idiopathic pneumonia syndrome ... Idiopathic pneumonia syndrome ... toxicity/Radiation pneumonitis ... thrombi - Radiation pneumonitis
Chronic hypersensitivity pneumonitis
The key findings in chronic hypersensitivity pneumonitis are:
Mosaic pattern with areas of ground-glass atenuation
hypersensitivity pneumonitis ... hypersensitivity pneumonitis ... hypersensitivity pneumonitis ... #Clinical #Radiology ... Hypersensitivity #Pneumonitis
Nodular pattern
1. Hypersensitivity pneumonitis: ill defined centrilobular nodules.
2. Miliary TB: random nodules
3. Sarcoidosis: nodules with perilymphatic
Hypersensitivity pneumonitis ... Hypersensitivity pneumonitis ... #Clinical #Radiology