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Kawasaki Disease (KD) - Diagnosis and Management Summary

Kawasaki Disease (KD) is the most common vasculitis of
the most common vasculitis ... Polymorphous rash ... #Disease #KD #vasculitis
Kawasaki Disease: Clinical Findings
Diagnostic Criteria - Fever and 4/5 of the following:
 • Conjunctivitis
 • Polymorphous
Conjunctivitis • Polymorphous ... Signs #Symptoms #Vasculitis
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... Cryoglobulinemic vasculitis ... syndrome • IgA vasculitis ... Small #Vessel #Vasculitides ... #vasculitis #differential
A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
A System for Vasculitides ... Diagnosis #IM #Rheum #Vasculitis
Vasculitis: In this instance, the vasculitic skin lesions were secondary to Haemophilus endocarditis.
Photo credit, Josh Fierer,
Vasculitis: In this ... instance, the vasculitic ... Dermatology #SkinRash #Vasculitis
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
Vasculitis - Break ... by large vessel vasculitis ... medium vessel vasculitis ... and small vessel vasculitis ... Large vessel vasculitis
Kawasaki Disease

Diagnostic criteria: 5-day fever PLUS four of the following…
 - 
Bilateral conjunctivitis
 - 
Cervical lymph
node >1.5cm - Polymorphous
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... When to Consider Vasculitis ... SMALL VESSEL VASCULITIS ... (anti-C1q Vasculitis ... #Vasculitides #
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... 50% Cutaneous Vasculitis ... Leukocytoclastic Vasculitis ... SLE, RA related vasculitis ... paraneoplastic Vasculitis
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
semiology of Cutaneous Vasculitis ... • Drug-induced vasculitis ... SLE +++ • IgA vasculitis ... • Necrotizing vasculitis ... Cryoglobulinemia vasculitis