2 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
enzyme, X-linked, Autoinflammatory ... , Somatic) Syndrome ... (MDS) Most met criteria ... #E1 #Xlinked #Autoinflammatory ... #Somatic #rheumatology
Idiopathic CD4 Lymphopenia (ICL) / Lymphocytopenia 

DIAGNOSTIC CRITERIA FOR ICL
 • Persistent CD4 T-cell lymphopenia
 •
Idiopathic CD4 Lymphopenia ... DIAGNOSTIC CRITERIA ... • Persistent CD4 ... chemotherapy) • Genetic syndromes ... ICL #diagnosis #hematology