3 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
enzyme, X-linked, Autoinflammatory ... : neutrophilic dermatosis ... (MDS) Most met criteria ... #E1 #Xlinked #Autoinflammatory ... #Somatic #rheumatology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
SAPHO syndrome is ... Etiology unknown: Autoinflammatory ... and neutrophilic dermatoses ... antibiotics with antiinflammatory ... #Rheumatology #
Diagnostic Criteria for Sweet Syndrome (Acute Febrile Neutrophilic Dermatosis)
Major criteria 
 1. Abrupt onset of tender
for Sweet Syndrome ... Febrile Neutrophilic Dermatosis ... neutrophils #Sweet #Syndrome ... #Neutrophilic #Dermatosis ... #Hematology #Dermatology