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Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
ANCA Associated ... polyangiitis - EGPA - GPA ... : • Temporal arteritis ... • Takayasu's arteritis ... #dermatology #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
vesicular eruption - Joints ... and branches • GCA ... aphthous ulcers, cutaneous ... strong sign of cutaneous ... differential #diagnosis #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Strong sign of cutaneous ... Elevated ESR and CRP GCA ... develop in pts with GCA ... vesicular eruption • Joints ... Palpable purpura, joint
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
: • Joint pain ... arthropathy • 90% joints ... vein thrombosis Hematologic ... Vasculitis: • ... anti-Ro/SSA can rule
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
arthralgia, and arthritis ... DDX: • ANCA (Antineutrophil ... - GPA, EGPA, microscopic ... Henoch-Schönlein purpura) • Cutaneous ... SLE), rheumatoid arthritis
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
Most common extra cutaneous ... and pain of the joints ... lymphoma, breast CA ... - Hematologic ... Leukocytoclastic vasculitis