11 results
X-Linked Agammaglobulinemia: Pathogenesis and clinical findings
The epidemiology of this disease is 1/340,000 births and roughly double
40% of patients diagnosed ... Signs of immunodeficiency ... > Inability to produce ... antibodies) -> Complete deficiency ... • Increased susceptibility
Spinal Cord Disorders - Differential Diagnosis Framework

Spinal cord neurological lesion:
Clinical findings:
 • Symptoms and signs below
- Differential Diagnosis ... • Symptoms and signs ... spasticity - Extensor ... Neurocysticercosis - Bacterial ... #neurology #differential
Blood Product Transfusions One Pager Summary
Type and screen - determines blood type and detects in recipient
recipients w/ IgA deficiency ... very rare), or bacterial ... - Bacterial ... #Transfusions #diagnosis ... #management #hematology
Weakness - Differential Diagnosis Framework

Approach To Weakness:
 • Non-neuromuscular disorder (Cardiac, pulmonary etc)
 • CNS ->
- Differential Diagnosis ... endocrine: Vitamin B12 deficiency ... Lack of UMN/LMN signs ... , CMV, EBV - Bacterial ... #neurology
Amyotrophic Lateral Sclerosis (ALS) Summary
ALS: combination of the clinical examination finding of amyotrophy with the pathologic
of UMN and LMN signs ... Clonus, Spasticity, Extensor ... EMG: LMN Signs in ... Lateral #Sclerosis #neurology ... #diagnosis #management
Blood Transfusion Reactions

Immune Mediated:
 • Febrile Non-Hemolytic Transfusion Reaction (FNHTR): Most common immune reaction to transfusion.
recipients w/ IgA deficiency ... very rare), or bacterial ... • Bacterial contamination ... #Transfusion #diagnosis ... #management #hematology
Sarcoidosis - Diagnosis and Management Summary
Epidemiology
1) High incidence in Scandinavian countries (11-24 cases per 100,000 individuals
Sarcoidosis - Diagnosis ... and Management ... activated macrophages produce ... erythema nodosum (extensor ... #Management #Signs
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
skin injury) • Neurologic ... Vascular Disease: Arterial ... artery aneurysms Diagnosis ... ) Differential Diagnosis ... #management #signs
Transverse Myelitis Overview

Focal inflammatory disorder of the spinal cord resulting in rapid onset of weakness, sensory
the legs and the extensors ... bouts of HTN Diagnostic ... • Bilateral signs ... • Nutritional Deficiency ... #management #neurology
Fluid Responsiveness and Fluid Tolerance Testing - OnePager Summary
Fluid resuscitation can be beneficial when required or
Arterial Line: ... measurement using arterial ... precede other signs ... Tolerance #testing #diagnosis ... comparison #challenges #management