4 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
Clinical Syndrome ... Features: alveolitis, ear ... peripheral blood myeloid ... cells NEJM Review ... Autoinflammatory #Somatic #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behçet's Syndrome ... pathognomonic laboratory ... Giant retinal tears ... #diagnosis #management ... signs #symptoms #rheumatology
Unilateral Floppy Eyelid Syndrome

This middle-aged male reported to clinic for persistent blurry vision and irritation of
Syndrome This ... Our management for ... Start artificial tears ... #Syndrome #FES ... #PhysicalExam #clinical
Clarkson’s Disease - Capillary leak syndrome
Epidemiology: Roughly 150 published cases, Median age 50 years, No sex
Capillary leak syndrome ... Laboratory features ... month at least 1 year ... #diagnosis #management ... timeline #treatment #rheumatology