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Congenital Heart Disorders - Classification and Differential Algorithm

- Amy Chung, MD, MSc @AmyChung 

#Congenital #Heart #Disorders
Congenital Heart Disorders ... Classification and Differential ... Congenital #Heart #Disorders ... Algorithm #Diagnosis #Peds ... #Pediatrics #Cardiology
Tetralogy of Fallot Summary
 • Anatomy
 • Incidence
 • Pathophysiology
 • Presentation
 • Common Variants
 •
• Incidence • Pathophysiology ... Associated Genetic Syndromes ... palliation • Post-Op Management ... Fallot #diagnosis #management ... #cardiology #peds
Causes of Developmental Delay - Differential Diagnosis Algorithm
Isolated Domain Delay - Reduced Respiratory Drive:
 • Cognitive
Developmental Delay - Differential ... Developmental Delay: • Syndromic ... Landau-Kleffner Syndrome ... DevelopmentalDelay #Differential ... Algorithm #Causes #Peds
Causes of Sudden Unexpected Death in Infancy (SUDI) - Differential Diagnosis Algorithm
Congenital Anomaly / Disorder:
 •
Infancy (SUDI) - Differential ... Congenital Anomaly / Disorder ... • Metabolic Disorders ... Sudden Infant Death Syndrome ... Algorithm #Causes #Peds
Causes of Enuresis - Differential Diagnosis Algorithm
Primary Nocturnal Enuresis (Urinary Control Never Achieved)
 • Delayed Maturation
of Enuresis - Differential ... Idiopathic • Sleep Disorders ... Bladder, Seizure Disorder ... Non-neurogenic (Hinman Syndrome ... Algorithm #Causes #Peds
Causes of Sudden Cardiac Arrest
Primary Myocardial Processes (> 90%):
 • Acquired structural heart disease: CAD, Most
, Brugada syndrome ... Drugs, Electrolyte disorders ... • WPW syndrome ... Cardiac #Arrest #cardiology ... #differential #
Aortic Stenosis & Bicuspid Aortic Valve (AS)
 • Introduction & Pathophysiology
 • Classifications
 • Epidemiology
 •
Introduction & Pathophysiology ... Pre-operative Management ... Post-operative Management ... #AorticValve #cardiology ... #peds #pediatrics
Acquired von Willebrand Syndrome - Diagnosis and Management
 • Autoantibodies to vWF: Lymphoproliferative disorders (e.g. lymphoma,
von Willebrand Syndrome ... Diagnosis and Management ... vonWillebrand #Syndrome ... #Diagnosis #Management ... treatment #hematology #differential
Etiologies of hypertrophic cardiomyopathy
 - Genetic 
 - Storage diseases 
 - Neuromuscular and mitochondrial disorders
mitochondrial disorders ... - Malformation syndromes ... cardiomyopathy #differential ... #diagnosis #cardiology
Atrioventricular Septal Defect
aka AV canal defect aka endocardial cushion defect
 • Epidemiology and Associations
 • Embryology
Physical Exam • Pathophysiology ... Post-Operative ICU Management ... cushion #diagnosis #management ... #peds #pediatrics ... #cardiology