2 results
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
Common Variable ... infection risk secondary ... to 8 years Clinical ... autoimmune hemolytic anemia ... DDX - Other causes
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
hyperinflammatory syndrome caused ... STX11, STXBP2 • Secondary ... Clinical Presentation ... • Common Signs ... - Cytopenias (anemia