5 results
Differentiation Syndrome in APML
Epidemiology:
 • Incidence: common in APL (2-48% depending on the study)
 • Triggers:
Triggers: ATRA treatment ... Prednisone 5mg/kg ... Renal Failure Treatment ... #diagnosis #management ... #hematology #oncology
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
aorta • Head and neck-limited ... Systemic (head and neck ... Glucocorticoids (0.6 mg/kg ... #management #phenotypes ... #rheumatology
Adult Onset Still's Disease
Systemic inflammation with urticarial rash.
Rash: 
 • Nonpruritic, evanescent (correlates with time of
Treatment - Mild ... : NSAIDS Treatment ... Prednisone 0.5-1mg/kg ... #rheumatology # ... management
Anti-NXP-2 Dermatomyositis

What?
DM with generalized subcutaneous edema
Pts have more myalgias, more severe weakness, and an increased prevalence
weakness in the neck ... positive patients Treatment ... Prednisone at 1 mg/kg ... #diagnosis #management ... #rheumatology #
Essential Thrombocythemia (ET)
ET is a chronic myeloproliferative neoplasm. Most cases are related to mutations that affect
Splenomegaly Diagnosis ... transformation into MDS or AML ... Thrombocythemia #ET #hematology ... #diagnosis #management ... #hematology