4 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
periventricular white matter ... CNS symptoms (headache ... disease) Differential ... • Nonsurgical abdominal ... diagnosis #management #signs
Rare Causes of Abdominal Pain
 • Hereditary Angioneurotic Edema - Recurrent visceral that may by swelling
the southern and eastern ... Mediterranean areas ... in the knee-to-chest ... Positive Carnett's sign ... #Pain #differential
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Vasculitis - Differential ... purpura: Strong sign ... 50 years • New headache ... gut involvement, abdominal ... vasculitis • Behcet
PFAPA Syndrome - Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Adenitis

EPIDEMIOLOGY:
PFAPA is the most common syndrome entailing
globally, excluding areas ... accompanied by headache ... DIFFERENTIAL DIAGNOSIS ... rashes, joint pain, headaches ... dominant inheritance pattern