102 results
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... cancers • Systemic diseases ... autoinflammatory diseases ... AdultOnset #Stills #Disease ... #diagnosis #management
Von Willebrand Disease - Clinical Presentation, Diagnosis and Management

- Dr. Eric Strong @DrEricStrong - Strong Medicine
Von Willebrand Disease ... - Clinical Presentation ... VonWillebrand #Disease ... #Diagnosis #Management ... #hematology #treatment
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Clinical Classification ... pulmonary disease ... multifactorial mechanisms Hematologic ... , Gaucher disease ... Classification #Diagnosis
Multifocal Atrial Tachycardia (MAT)
• At least 3 different P wave morphologies: 
• Rate 100-180
• Irregular 
Etiology
to chronic lung disease ... • Hypoxia • Pulmonary ... Tachycardia #MAT #Cardiology ... #Diagnosis #ECG ... #EKG #Management
Antinuclear Antibodies (ANA)
ANA or Anti-NucIear Antibody refers to antibodies against antigens in the nucleus → like
ANA ≠ Autoimmune Disease ... likely it will be clinically ... • Rheumatic Diseases ... , Interstitial Pulmonary ... #diagnosis #differential
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
life-threatening diseases ... Inflammatory eye disease ... Anti-GBM antibody • Urine ... : UA, Urine protein ... #management #treatment
Leptospirosis
Pathogen: Leptospira (interrogans, kirschneri, noguchii)
Risk Factors:
 • Occupational exposure - Farmers, ranchers, trappers, veterinarians
 • Recreational
Presentation: • Mild disease ... Meningitis • Weil's Disease ... failure • Severe pulmonary ... disease ARDS Diagnosis ... #treatment #management
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
• Chronic lung disease ... Granulomatous disease ... • Liver diseases ... interstitial lung disease ... #diagnosis #management
Hematuria in Post-Renal Transplant Patient
Prevalence up to 12% in the postrenal transplant patient
 • Bacterial: Escherichia
, Busulfan • Disease ... #differential #diagnosis ... kidney #blood #urine ... #management #treatment ... #nephrology
Blastomycosis (Blastomyces): Gilchrist’s disease, Chicago disease - Summary Sheet
 • Morphology
 • Geography, Reservoir and Mode
): Gilchrist’s disease ... , Chicago disease ... inoculation • Clinical ... Extrapulmonary disease ... - Pulmonary disease