5 results
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... alveolar hemorrhage + Glomerulonephritis ... polyangiitis, Microscopic ... sclerosis • Anti-Glomerular ... anti-ANCA ab, anti-GBM
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Pulmonary Renal ... polyangiitis), MPA (microscopic ... antibody, Anti-GBM ... usually low in anti-GBM ... hypercellular glomeruli
Anti-GIomeruIar Basement Membrane Disease (Goodpasture's Disease)

What is it? A small vessel vasculitis with circulating antibodies directed
directed against the glomerular ... rapidly progressive glomerulonephritis ... Diagnosis: • Anti-GBM ... AntiGBM #diagnosis #nephrology ... #pulmonary
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
and renal abnormalities ... PR3-ANCA): • Microscopic ... ) • Anti-GBM - ... : - Kidneys: glomerular ... • Urinalysis (Renal
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
and renal abnormalities ... • Kidneys: Non-glomerular ... (PR3-ANCA)): Microscopic ... , pauci-immune glomerulonephritis ... pain and GN Anti-GBM