45 results
Lab patterns seen in Inborn Errors of Metabolism

A table of lab values compiled from UpToDate and
Metabolism A table ... See IEM schema for ... metabolicemergency-pathophysiology-differential-pediatrics-metabolism-algorithm-diagnosis ... #Neonatology #Peds ... #Pediatrics #Table
Inherited Qualitative Platelet Defects
Bernard-Soulier Syndrome
 • Defect of adhesion due to a lack of GP Ib/IX/V
Qualitative Platelet Defects ... of GP Ib/IX/V [vWF ... Thrombasthenia • Defect ... α-granules (contains vWF ... #comparison #table
A schema of the pathophysiology of the inborn errors of metabolism, excluding complex storage diseases. Helps
the lab values table ... Pathophysiology #Diagnosis #Algorithm ... #Neonatology #Peds ... #Pediatrics #Table ... #IEM #NICU #InbornErrors
Cardiac Murmurs and Maneuvers

An algorithm demonstrating the effect of various maneuvers on systolic murmurs. 
TR, tricuspid
Maneuvers An algorithm ... demonstrating the effect ... aortic stenosis; VSD ... ventricular septal defect ... The effect of squatting
Catecholamine Vasopressor Effect Sites and Indications #Pathophys #Management #EM #IM #PCC #Catecholamine #Comparison #Table #Epi #Norepi
Catecholamine Vasopressor Effect ... Pathophys #Management #EM ... #IM #PCC #Catecholamine ... #Comparison #Table
Causes of Cyanosis in the Newborn - Differential Diagnosis Algorithm
Peripheral Only:
 • Poor Perfusion
 • Acrocyanosis
Hemoglobinopathy:
Differential Diagnosis Algorithm ... Ventricular Septal Defect ... Atrial Septal Defect ... Differential #Diagnosis #Algorithm ... #Causes #Peds #
Tetralogy of Falot on Chest X-Ray
Tetralogy of Falot comprises four defects -
1. Ventricular septal defect (VSD)
2.
comprises four defects ... Ventricular septal defect ... (VSD) 2. ... clinical #radiology #peds
Undifferentiated critical congenital heart disease: Patterns of Presentation 
Pink baby:
 • Presents at 1-6 mo
R shunt: PDA, VSD ... , AV canal defect ... catch blue baby defects ... Blue #Gray #Baby #Peds
Jaundice Evaluation Algorithm #Diagnosis #Management #EM #IM #GI #Jaundice #Hyperbilirubinemia #Workup #Evaluation #Differential #Algorithm #Direct #Indirect
Jaundice Evaluation Algorithm ... Diagnosis #Management #EM ... #IM #GI #Jaundice ... #Differential #Algorithm ... #Direct #Indirect
PEMSource: Algorithm for fever WITHOUT source by Age
#Diagnosis #Management #Peds #Fever #Without #Source #Table #Algorithm #PEMSource
PEMSource: Algorithm ... Diagnosis #Management #Peds ... Without #Source #Table ... #Algorithm #PEMSource