13 results
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
- Diagnosis, causes ... Clinical manifestations ... neuropathy Treatment ... with refractory disease ... #Rheumatology #
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... and diplopia) • Vascular ... Behcet syndrome (Clinical ... Arthritis, AS Treatment ... signs #symptoms #rheumatology
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
• They can cause ... Vascular Sludging ... Syndrome: • Clinical ... • Autoimmune diseases ... classification #rheumatology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Hyperviscosity, - Vascular ... malignancies, vasculitis ... Diagnosis: • + Clinical ... cryoglobulins • Negative causes ... Cryofibrinogenemia #diagnosis #rheumatology
Endocarditis - Overview and Differential Diagnosis Framework

Who?
Infectious:
• Pre-existing valvular disease
• Prosthetic valve
• Congenital heart disease
• IV
valvular disease ... • Vasculitis ... Septic emboli cause ... hematuria, + RF Treatment ... Differential #Diagnosis #cardiology
Clarkson’s Disease - Capillary leak syndrome
Epidemiology: Roughly 150 published cases, Median age 50 years, No sex
150 published cases ... Relapsing-remitting course +++ Clinical ... IVIg) • Limit vascular ... spacing of IVIg cures ... #rheumatology
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
Hypocomplementemia • Can cause ... salivary ducts Clinical ... ) • Cutaneous vasculitis ... Adenocarcinoma Treatment ... Sjogrens #Syndrome #Rheumatology
Wegener's granulomatosis
Wegener's is a collagen vascular disease with vasculitis involving the lung, kidney and sinuses.
In the
is a collagen vascular ... disease with vasculitis ... In the lung the vasculitis ... causes infarcts ... #Clinical #Radiology
Polymyalgia Rheumatica (PMR) Diagnosis and Management Summary

WHAT?
 • Polymyalgia rheumatica (PMR) is a common systemic inflammatory
of unknown cause ... CLINICAL: • Physical ... universally used, ultrasound ... TREATMENT: • The ... Diagnosis #Management #Rheumatology
Peripartum Cardiomyopathy - Summary
1. Definition
 • Towards the end of pregnancy to 5 months postpartum
exclude other causes ... or dilated) • Valvular ... support for patients clinically ... diagnosis #management #cardiology ... #treatment