Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group
< 5% of mixed cryoglobulinemia vasculitis
Clinical manifestations
- Skin involvement with purpura
- Renal involvement
- Joint involvement
- Less peripheral neuropathy
Treatment
- Specific anti-infectious therapy as first-line therapy are associated with sustained remission
- Refractory or relapsing patients are frequently related to HBV infection
- GCs and/or IS agents used in the absence of anti-infectious agents are frequently associated with refractory disease
Dr. Benjamin Terrier @ https://twitter.com/TerrierBen
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