2788 results
X-linked Severe Combined Immunodeficiency (SCID): Pathogenesis and clinical findings

#SCID #SevereCombinedImmunodeficiency #XLinked #pathophysiology #immunology
X-linked Severe ... SevereCombinedImmunodeficiency #XLinked
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
, E1 enzyme, X-linked ... #Vacuoles #E1 #Xlinked
Comparison of Causes of Salt-Wasting in Infancy
 - PHA 1
 - PHA 3
 - 21-OH CAH
21-OH CAH - X-Linked
X-Linked Agammaglobulinemia: Pathogenesis and clinical findings
The epidemiology of this disease is 1/340,000 births and roughly double
X-Linked Agammaglobulinemia ... Agammaglobulinemia #XLinked
Flowchart to diuretic use in acute heart failure.

(A) Congestion with volume overload. 

(B) Treatment algorithm after
sodium–glucose linked ... HeartFailure #Cardiology #Management
Beautiful acanthocytes/spur cells in a patient with McLeod Syndrome. X-linked disorder characterized by reduced expression of
X-linked disorder
Capnography Waveforms
Sudden loss of waveform
 • ET tube disconnected, dislodged, kinked or obstructec
 • Loss of
disconnected, dislodged, kinked
The Cribsiders episode: "Cystic Fibrosis Licked-ty Split with Dr. Whittney Warren" 

#cysticfibrosis #cftr #pediatrics #podcast #education
Cystic Fibrosis Licked-ty
Pain Assessment and Management Initiative (PAMI) - Pain Management and Dosing Guide

#Management #Pain #Pharmacology #Doses #Dosing
Assessment and Management ... (PAMI) - Pain Management ... Dosing Guide #Management
Acute Kidney Injury - Differential Diagnosis Framework
PRERENAL:
 - Intrarenal vasoconstriction-hemodynamically mediated
 - Systemic vasodilation
 - Volume
urinalysis, labs - Management ... renal biopsy - Management ... ultrasonography - Manaqement