11 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... skin injury) • Neurologic ... Medium and large also ... disease (SVC/IVC occlusion ... signs #symptoms #rheumatology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
pulmonary emboli, and ocular ... thrombi including retinal ... and/or venous occlusions ... , as well as gangrene ... Antiphospholipid syndrome
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
et diutinum Neurologic ... Hypergammaglobulinemic macular ... vascular beds-renal ... , retinal, DVT, ... Paraproteinemias #Hematology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
ulcers, cutaneous, ocular ... • Cogan Syndrome ... : - Ocular inflammatory ... reactions, and vaso-occlusive ... differential #diagnosis #rheumatology
Locked-in Syndrome (LiS) in ALS

What happens when ALS patients opt for mechanical ventilation? They can become
Locked-in Syndrome ... (LiS) in ALS ... #LockedIin #Syndrome ... #video #physicalexam ... #ocular #neurology
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
Differential Diagnosis Neurologic-Centered ... Features: POEMS, AL ... capillary leak syndrome ... • Schnitzler syndrome ... Cryoglobulinemia Renal-centered
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
pulmonary and renal ... reactions, and vaso-occlusive ... affects the skin, neurologic ... cognitive impairment, neurologic ... Differential #Diagnosis #Rheumatology
Orbital Apex Syndrome secondary to Herpes Zoster Ophthalmicus (HZO)

This 81 yo male was referred to our
Orbital Apex Syndrome ... acetate to help with ocular ... 10mg/kg/8hr and also ... ophthalmology #physicalexam ... #neurology
The Neurological Evaluation of a Comatose Patient

Definition:
 • Coma: a state of unresponsiveness; the absence of
Unresponsive wakefulness syndrome ... • Locked-in syndrome ... • Vestibulo-ocular ... caseyalbin #PhysicalExam ... #neurology #comatose
Opsoclonus Myoclonus Syndrome (OMS) on Physical Exam

Opsoclonus: Rapid, repetitive conjugate involuntary chaotic multidirectional (horizontal, vertical, and
Opsoclonus Myoclonus Syndrome ... OMS can occur as ... #PhysicalExam # ... ocular #clinical ... #video #eyes #neurology