8 results
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
) Pathophysiology ... sIL-2R >2400 Ul/ml ... • Autoimmune diseases ... Adult-onset Still disease ... #management #treatment
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
age, however the disease ... : HLH signs and ... Diagnosis via genetic ... Ferritin >500 ng/mL ... #management #treatment
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
common in Asia • HLA-B51 ... artery aneurysms Diagnosis ... ) Differential Diagnosis ... Behcet #Syndrome #diagnosis ... #management #signs
Rheumatoid arthritis (RA): Pathogenesis and Joint diseases features
 • RA affects 1% of population, women >
Pathogenesis and Joint diseases ... Extra-articular signs ... RheumatoidArthritis #RA #pathophysiology ... #signs #symptoms ... #diagnosis
Amyotrophic Lateral Sclerosis (ALS) Summary
ALS: combination of the clinical examination finding of amyotrophy with the pathologic
clinical examination finding ... the pathologic finding ... lateral sclerosis Pathophysiology ... Presentation: - Disease ... #management
Stiff Person Syndrome (SPS) - Diagnosis and Management Summary

Epidemiology:
 • Prevalence: 1-2 cases per million -
and Management ... Person Syndrome Pathophysiology ... to diazepam or findings ... testing Lab Findings ... #Management #treatment
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
recognition and management ... ▪ Autoimmune diseases ... Presentation • Common Signs ... Pathophysiology ... #Management #Hematology
Transverse Myelitis Overview

Focal inflammatory disorder of the spinal cord resulting in rapid onset of weakness, sensory
monophasic Pathophysiology ... compression (MRI) and findings ... bouts of HTN Diagnostic ... • Bilateral signs ... #management #neurology