14 results
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Clinical triad ... decreased glycosylated fraction ... #diagnosis #management ... #treatment #rheumatology
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Fever is the main clinical ... rash) • Heart, lung ... thrombocytopenia • Liver function ... Syndrome #Diagnosis #Management ... #Hematology #Rheumatology
Nutrition in Cirrhosis: Dos and Don’ts
Screening:
 • Patients at risk for RFH-Nutritional Prioritizing Tool
 • Low
Analysis, muscle ultrasound ... ) • Muscle function ... pattern (avoiding long ... muscle mass and function ... Cirrhosis #diet #management
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
to 8 years Clinical ... • Chronic lung ... lymphocytic interstitial lung ... and M panel Management ... #diagnosis #management
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... Clinical history ... biliary, renal, lung ... #diagnosis #management ... workup #treatment #rheumatology
Portopulmonary Hypertension
Presence of pulmonary arterial hypertension in a patient with portal hypertension
No other obvious causes (chronic
causes (chronic lung ... disease, left heart ... disease, thromboembolism ... Transthoracic echocardiogram ... Hypertension #diagnosis #management
Chronic Thromboembolic Pulmonary Hypertension (CTEPH) and Pulmonary Thromboendarterectomy
Chronic Thromboembolic Pulmonary Hypertension
Definition: mean pulmonary-artery pressure > 25mmHg
Plexiform-lesion formation Clinical ... Ventilation-perfusion lung ... have inoperable disease ... variables, WHO functional ... Thromboendarterectomy #diagnosis #management
Myasthenic Crisis Checklist - Myasthenia Gravis

Evaluation 
 - Chest X-ray and lung ultrasound (exclude other lung
Chest X-ray and lung ... ultrasound (exclude ... other lung disease ... (vital signs, clinical ... MyastheniaGravis #Checklist #Management
Heart failure with Reduced Ejection Fraction (HFrEF)
Clinical Presentation
1. Typical symptoms: dyspnea, orthopnea paroxysmal noctumal dyspnea, fatigue,
Reduced Ejection Fraction ... (HFrEF) Clinical ... : weight gain, lung ... coronary artery disease ... heartfailure #diagnosis #management
Preoperative Risk Evaluation

Major Pre-Op Questions:
1. Does the patient have any modifiable risk factors that could be
Assess functional ... Functional status ... Change in clinical ... unless prior heart/lung ... medical and surgical management