14 results
2021 ACR/VF Guidelines for Management of Eosinophilic Granulomatosis with Polyangiitis (EGPA)

#EGPA #Eosinophilic #Granulomatosis #Polyangiitis #ACR2021 #Management
Guidelines for Management ... of Eosinophilic Granulomatosis ... #Eosinophilic #Granulomatosis ... #rheumatology # ... algorithm #vasculitis
2021 ACR/VF Guidelines for Management of Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA)

#Granulomatosis #Polyangiitis #GPA
Guidelines for Management ... of Granulomatosis ... #MPA #ACR2021 #Management ... #rheumatology # ... algorithm #vasculitis
Proposed Treatment Algorithm for MAS / HLH

#MAS #HLH #Hemophagocytic #Lymphohistiocytosis #Management #Treatment #Algorithm #Hematology
Proposed Treatment Algorithm ... Hemophagocytic #Lymphohistiocytosis ... #Management #Treatment ... #Algorithm #Hematology
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Nodosa (PAN) • Granulomatosis ... • Eosinophilic Granulomatosis ... ACR2021 #Guidelines #algorithm ... #rheumatology
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Granulomatosis with ... ANCA Vasculitis Management ... Algorithm - ACR ... ANCA #Vasculitis #Management ... #rheumatology
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
Malabsorption • Granulomatous ... breast cancer Granulomatous ... and M panel Management ... hypogammaglobulinemia #immunology #hematology ... #diagnosis #management
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Eosinophilic Granulomatosis ... ANCA Vasculitis Management ... Algorithm - ACR ... ANCA #Vasculitis #Management ... #rheumatology
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
Hemophagocytic Lymphohistiocytosis ... • Autoimmune diseases ... Adult-onset Still disease ... #diagnosis #management ... treatment #summary #rheumatology
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
haemophagocytic lymphohistiocytosis ... hemophagocytic lymphohistiocytosis ... highly inflammatory disease ... Syndrome #Diagnosis #Management ... #Hematology #Rheumatology
Polyarteritis Nodosa (PAN) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Severe Disease → Remission
) - Vasculitis Management ... Algorithm - ACR ... Guidelines • Severe Disease ... • Non-Severe Disease ... #rheumatology